TY - CHAP M1 - Book, Section TI - Double Outlet Right Ventricle A1 - Bianchi, Diana W. A1 - Crombleholme, Timothy M. A1 - D'Alton, Mary E. A1 - Malone, Fergal D. PY - 2015 T2 - Fetology: Diagnosis and Management of the Fetal Patient, 2e AB - Key PointsDouble outlet right ventricle (DORV) is a complex cardiac malformation in which the majority of both pulmonary and aortic trunks arise from the right ventricle, typically coexisting with a VSD.While DORV represents a heterogeneous group of abnormalities with various classification systems, a combined anatomic-surgical classification system is now used as it predicts optimal surgical intervention.Prenatal diagnosis depends on accurate delineation of the outflow tract paths, including localizing the VSD.The majority of cases have associated cardiac malformations, abnormalities of organ situs, or chromosomal abnormalities.Because of the variable clinical presentation at birth, delivery should occur in controlled circumstances at a center with pediatric cardiology backup available, and the ability to begin a prostaglandin infusion.Definitive surgical correction should occur during the first year of life, with most cases achieving a biventricular repair using an intraventricular tunnel. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/04/23 UR - obgyn.mhmedical.com/content.aspx?aid=1106398233 ER -