RT Book, Section
A1 Bianchi, Diana W.
A1 Crombleholme, Timothy M.
A1 D'Alton, Mary E.
A1 Malone, Fergal D.
SR Print(0)
ID 1106399360
T1 Multicystic Dysplastic Kidney
T2 Fetology: Diagnosis and Management of the Fetal Patient, 2e
YR 2015
FD 2015
PB McGraw-Hill Education
PP New York, NY
SN 978-0-07-144201-5
LK obgyn.mhmedical.com/content.aspx?aid=1106399360
RD 2024/04/24
AB Key  PointsMulticystic  dysplastic  kidney  (MCDK)  is  a  severe  renal  abnormality  associated  with  atretic  ureter  and  absence  of  normal  renal  parenchyma,  which  is  replaced  by  multiple  large  noncommunicating  cysts.MCDK  is  generally  easily  diagnosed  prenatally,  often  due  to  the  large  size  of  the  kidney  and  its  constituent  cysts.It  is  usually  unilateral,  while  the  rare  cases  of  bilateral  MCDK  present  as  Potters  syndrome.In  almost  half  of  the  cases  of  unilateral  MCDK,  the  contralateral  kidney  will  have  associated  malformations,  the  severity  of  which  determines  the  overall  prognosis.Management  of  pregnancy  and  delivery  generally  does  not  need  to  be  changed  following  the  prenatal  diagnosis  of  MCDK.While  some  cases  of  unilateral  MCDK  will  regress  prenatally  or  in  pediatric  life,  there  is  no  agreement  on  need  for  nephrectomy  in  those  cases  with  persistent  MCDK.MCDK  greater  than  6  cm,  cases  in  which  the  MCDK  obstructs  the  diaphragm  or  gastrointestinal  tract,  or  cases  in  which  hypertension  develops  will  generally  require  nephrectomy.