TY - CHAP M1 - Book, Section TI - Cystic Adenomatoid Malformation A1 - Bianchi, Diana W. A1 - Crombleholme, Timothy M. A1 - D'Alton, Mary E. A1 - Malone, Fergal D. PY - 2015 T2 - Fetology: Diagnosis and Management of the Fetal Patient, 2e AB - Key PointsCCAM is cystic malformation of pulmonary tissue and, unlike BPS, typically has a pulmonary blood supply.CCAM has been subdivided into five types, depending on the number and size of cystic changes; additionally hybrid lesions in which features of BPS coexist have been described.Prenatal ultrasound can detect either cystic or solid mass in the chest without a systemic vascular supply.Differential diagnosis includes BPS, diaphragmatic hernia, and bronchogenic cyst.Cases of CCAM with a dominant large cyst, or with a CCAM volume ratio greater than 1.6, appear to be at most risk of developing hydrops in utero, which is associated with very poor prognosis; in contrast, some cases of CCAM also regress spontaneously in utero.Fetal intervention is possible by means of thoracoamniotic shunting for cases of hydrops with a dominant cyst, or by means of open fetal surgical resection for cases of hydrops with a microcystic appearance; additionally a course of antenatal corticosteroids may also be beneficial.Delivery should occur electively, at term, in a tertiary care center with adequate pediatric surgical facilities available. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/29 UR - obgyn.mhmedical.com/content.aspx?aid=1106397448 ER -