TY - CHAP M1 - Book, Section TI - Ebstein Anomaly A1 - Bianchi, Diana W. A1 - Crombleholme, Timothy M. A1 - D'Alton, Mary E. A1 - Malone, Fergal D. PY - 2015 T2 - Fetology: Diagnosis and Management of the Fetal Patient, 2e AB - Key PointsEbstein anomaly is a malformation of the tricuspid valve, causing tricuspid insufficiency and atrialization of a significant portion of the right ventricle.When it progresses it can be associated with right ventricular outflow tract obstruction and arrhythmias.It is rarely associated with extracardiac malformations or fetal aneuploidy.Prognosis for prenatally diagnosed cases is much worse than for those diagnosed later in childhood, with less than 50% of cases surviving to 5 years of age.Pregnancy management rarely needs to be altered significantly, other than to arrange for prompt referral for postnatal cardiac evaluation and likely surgical repair, either by means of valve repair or replacement. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/04/18 UR - obgyn.mhmedical.com/content.aspx?aid=1106397952 ER -