TY  - CHAP
M1  - Book, Section
TI  - Hypoplastic Left Ventricle
A1  - Bianchi, Diana W.
A1  - Crombleholme, Timothy M.
A1  - D'Alton, Mary E.
A1  - Malone, Fergal D.
PY  - 2015
T2  - Fetology: Diagnosis and Management of the Fetal Patient, 2e
AB  - Key  PointsHypoplastic  left  heart  syndrome  (HLHS)  is  a  spectrum  of  disorders  involving  aortic  atresia  with  or  without  mitral  atresia  or  stenosis.The  condition  may  be  diagnosed  as  severe  ventricular  hypoplasia  before  20  weeks’  gestation,  or  it  may  evolve  from  aortic  stenosis  to  HLHS  during  the  second  half  of  pregnancy.Prenatal  diagnosis  of  classic  HLHS  is  straightforward  as  the  ventricular  disproportion  is  obvious,  leading  to  prenatal  detection  rates  as  high  as  85%.Delivery  needs  to  be  carefully  planned  to  optimize  the  availability  of  pediatric  specialists,  and  will  include  immediate  prostaglandin  infusion  and  referral  to  cardiothoracic  surgeons  for  initial  palliation.Surgical  management  includes  a  choice  between  traditional  three-stage  Norwood  procedure  leading  ultimately  to  a  single  ventricle  repair,  versus  hybrid  palliation  involving  open  surgical  and  interventional  catheterization  until  cardiac  transplantation  is  available.  
SN  - 
PB  - McGraw-Hill Education
CY  - New York, NY
Y2  - 2024/04/19
UR  - obgyn.mhmedical.com/content.aspx?aid=1106398028
ER  -