RT Book, Section
A1 Bianchi, Diana W.
A1 Crombleholme, Timothy M.
A1 D'Alton, Mary E.
A1 Malone, Fergal D.
SR Print(0)
ID 1106396480
T1 Hydranencephaly
T2 Fetology: Diagnosis and Management of the Fetal Patient, 2e
YR 2015
FD 2015
PB McGraw-Hill Education
PP New York, NY
SN 978-0-07-144201-5
LK obgyn.mhmedical.com/content.aspx?aid=1106396480
RD 2024/04/16
AB Key  PointsHydranencephaly  is  a  rare  condition  in  which  the  cerebral  hemispheres  are  virtually  absent.The  typical  case  is  that  of  an  isolated  finding  without  additional  abnormalities.The  diagnosis  should  be  expected  when  a  large  cystic  mass  fills  the  cranial  cavity  and  there  is  no  recognizable  cerebral  cortex.The  antenatal  natural  history  is  not  well  known  but  appears  to  represent  an  evolving  intrauterine  process  secondary  to  a  vascular  insult.Correct  diagnosis  is  important  for  the  management  of  these  cases.  Vaginal  delivery  is  optimal.The  long-term  outcomes  associated  with  complete  hydranencephaly  are  extremely  poor.In  most  cases,  there  is  no  recurrence  risk  since  hydranencephaly  is  most  often  associated  with  a  destructive  process  rather  than  with  a  primary  malformation.