RT Book, Section
A1 Bianchi, Diana W.
A1 Crombleholme, Timothy M.
A1 D'Alton, Mary E.
A1 Malone, Fergal D.
SR Print(0)
ID 1106397397
T1 Bronchopulmonary Sequestration
T2 Fetology: Diagnosis and Management of the Fetal Patient, 2e
YR 2015
FD 2015
PB McGraw-Hill Education
PP New York, NY
SN 978-0-07-144201-5
LK obgyn.mhmedical.com/content.aspx?aid=1106397397
RD 2024/10/10
AB Key  PointsBronchopulmonary  sequestration  (BPS)  is  a  mass  of  nonfunctioning  lung  tissue  that  does  not  communicate  with  the  bronchial  tree.Prenatal  diagnosis  is  possible  by  noting  an  echodensetriangulararea  of  tissue,  often  with  an  obvious  systemic  feeding  vessel,  such  as  from  the  descending  aorta.BPS  can  be  intralobar  (same  pleural  cover  as  normal  lung)  or  extralobar  (separate  pleural  cover),  and  can  be  intrathoracic  or  extrathoracic.Main  differential  diagnosis  for  intrathoracic  BPS  includes  type  III  CCAM,  teratoma,  and  diaphragmatic  hernia,  while  the  differential  for  intra-abdominal  BPS  includes  mesoblastic  nephroma  and  neuroblastoma.At  least  75%  of  prenatally  diagnosed  cases  of  BPS  resolve  spontaneously,  while  those  associated  with  hydrops,  pleural  effusions,  or  mediastinal  shift  have  a  much  worse  prognosis.Fetal  intervention  by  means  of  thoracoamniotic  shunting  may  be  an  option  for  cases  with  coexisting  pleural  effusions  prior  to  30  weeks'  gestation.For  large  lesions  that  persist  prenatally,  and  for  those  associated  with  hydrops,  delivery  should  occur  in  a  tertiary  care  center.Elective  surgical  excision  is  recommended  for  most  cases  of  asymptomatic  BPS  that  persist  postnatally.