RT Book, Section A1 Bianchi, Diana W. A1 Crombleholme, Timothy M. A1 D'Alton, Mary E. A1 Malone, Fergal D. SR Print(0) ID 1106397448 T1 Cystic Adenomatoid Malformation T2 Fetology: Diagnosis and Management of the Fetal Patient, 2e YR 2015 FD 2015 PB McGraw-Hill Education PP New York, NY SN 978-0-07-144201-5 LK obgyn.mhmedical.com/content.aspx?aid=1106397448 RD 2024/03/28 AB Key PointsCCAM is cystic malformation of pulmonary tissue and, unlike BPS, typically has a pulmonary blood supply.CCAM has been subdivided into five types, depending on the number and size of cystic changes; additionally hybrid lesions in which features of BPS coexist have been described.Prenatal ultrasound can detect either cystic or solid mass in the chest without a systemic vascular supply.Differential diagnosis includes BPS, diaphragmatic hernia, and bronchogenic cyst.Cases of CCAM with a dominant large cyst, or with a CCAM volume ratio greater than 1.6, appear to be at most risk of developing hydrops in utero, which is associated with very poor prognosis; in contrast, some cases of CCAM also regress spontaneously in utero.Fetal intervention is possible by means of thoracoamniotic shunting for cases of hydrops with a dominant cyst, or by means of open fetal surgical resection for cases of hydrops with a microcystic appearance; additionally a course of antenatal corticosteroids may also be beneficial.Delivery should occur electively, at term, in a tertiary care center with adequate pediatric surgical facilities available.