RT Book, Section
A1 Bianchi, Diana W.
A1 Crombleholme, Timothy M.
A1 D'Alton, Mary E.
A1 Malone, Fergal D.
SR Print(0)
ID 1106397952
T1 Ebstein Anomaly
T2 Fetology: Diagnosis and Management of the Fetal Patient, 2e
YR 2015
FD 2015
PB McGraw-Hill Education
PP New York, NY
SN 978-0-07-144201-5
LK obgyn.mhmedical.com/content.aspx?aid=1106397952
RD 2024/04/25
AB Key  PointsEbstein  anomaly  is  a  malformation  of  the  tricuspid  valve,  causing  tricuspid  insufficiency  and  atrialization  of  a  significant  portion  of  the  right  ventricle.When  it  progresses  it  can  be  associated  with  right  ventricular  outflow  tract  obstruction  and  arrhythmias.It  is  rarely  associated  with  extracardiac  malformations  or  fetal  aneuploidy.Prognosis  for  prenatally  diagnosed  cases  is  much  worse  than  for  those  diagnosed  later  in  childhood,  with  less  than  50%  of  cases  surviving  to  5  years  of  age.Pregnancy  management  rarely  needs  to  be  altered  significantly,  other  than  to  arrange  for  prompt  referral  for  postnatal  cardiac  evaluation  and  likely  surgical  repair,  either  by  means  of  valve  repair  or  replacement.