RT Book, Section A1 Bianchi, Diana W. A1 Crombleholme, Timothy M. A1 D'Alton, Mary E. A1 Malone, Fergal D. SR Print(0) ID 1106397986 T1 Hypoplastic Right Ventricle T2 Fetology: Diagnosis and Management of the Fetal Patient, 2e YR 2015 FD 2015 PB McGraw-Hill Education PP New York, NY SN 978-0-07-144201-5 LK obgyn.mhmedical.com/content.aspx?aid=1106397986 RD 2024/03/18 AB Key PointsHypoplastic right ventricle is considerably rarer than hypoplastic left heart syndrome.It is a complex cardiac malformation with a wide spectrum of presentations, the most serious of which frequently results in a single-ventricle functionality.Prenatal sonographic features include pulmonary atresia with an intact ventricular septum, varying degrees of tricuspid atresia and tricuspid regurgitation, and varying degrees of hypoplasia of the right ventricular walls.Neonates will be ductal-dependent and therefore delivery should be carefully coordinated in a center that can provide immediate pediatric cardiology intervention, prostaglandin infusion to maintain a patent ductus arteriosus, and ability to provide prompt catheter-based interventions such as pulmonary valvotomy, ductus arteriosus stenting, and balloon atrial septostomy.Optimal management is individualized between catheter-based approaches that allow blood flow from right to left sides of the heart, together with open surgical systemic-pulmonary shunting.Long-term outcome depends on whether a biventricular or univentricular repair is achieved.