RT Book, Section
A1 Bianchi, Diana W.
A1 Crombleholme, Timothy M.
A1 D'Alton, Mary E.
A1 Malone, Fergal D.
SR Print(0)
ID 1106398233
T1 Double Outlet Right Ventricle
T2 Fetology: Diagnosis and Management of the Fetal Patient, 2e
YR 2015
FD 2015
PB McGraw-Hill Education
PP New York, NY
SN 978-0-07-144201-5
LK obgyn.mhmedical.com/content.aspx?aid=1106398233
RD 2024/04/20
AB Key  PointsDouble  outlet  right  ventricle  (DORV)  is  a  complex  cardiac  malformation  in  which  the  majority  of  both  pulmonary  and  aortic  trunks  arise  from  the  right  ventricle,  typically  coexisting  with  a  VSD.While  DORV  represents  a  heterogeneous  group  of  abnormalities  with  various  classification  systems,  a  combined  anatomic-surgical  classification  system  is  now  used  as  it  predicts  optimal  surgical  intervention.Prenatal  diagnosis  depends  on  accurate  delineation  of  the  outflow  tract  paths,  including  localizing  the  VSD.The  majority  of  cases  have  associated  cardiac  malformations,  abnormalities  of  organ  situs,  or  chromosomal  abnormalities.Because  of  the  variable  clinical  presentation  at  birth,  delivery  should  occur  in  controlled  circumstances  at  a  center  with  pediatric  cardiology  backup  available,  and  the  ability  to  begin  a  prostaglandin  infusion.Definitive  surgical  correction  should  occur  during  the  first  year  of  life,  with  most  cases  achieving  a  biventricular  repair  using  an  intraventricular  tunnel.