RT Book, Section A1 Bianchi, Diana W. A1 Crombleholme, Timothy M. A1 D'Alton, Mary E. A1 Malone, Fergal D. SR Print(0) ID 1106398280 T1 Truncus Arteriosus T2 Fetology: Diagnosis and Management of the Fetal Patient, 2e YR 2015 FD 2015 PB McGraw-Hill Education PP New York, NY SN 978-0-07-144201-5 LK obgyn.mhmedical.com/content.aspx?aid=1106398280 RD 2024/03/29 AB Key PointsTruncus arteriosus is a rare form of congenital cardiac disease in which a single cardiac outflow tract gives rise to the pulmonary, coronary, and systemic circulations.Prenatal diagnosis relies upon failure to visualize three separate vessels in a transverse view through the upper mediastinum, and failure to visualize the normal branch pulmonary arteries and their origin from the right ventricle.Up to 40% of cases are associated with a 22q11 deletion and the DiGeorge syndrome, thereby making amniocentesis a crucial part of the prenatal diagnostic evaluation.While timing and mode of delivery do not need to be altered following the diagnosis, planned delivery in a tertiary care setting with appropriate pediatric cardiology backup is critical, as congestive cardiac failure can occur in the neonatal period.Early definitive surgical repair is recommended, typically by means of a homograft from the right ventricle to the pulmonary artery, with closure of a VSD.Long-term survival rates of 80% can be expected.