RT Book, Section
A1 Bianchi, Diana W.
A1 Crombleholme, Timothy M.
A1 D'Alton, Mary E.
A1 Malone, Fergal D.
SR Print(0)
ID 1106398374
T1 Heterotaxy Syndrome
T2 Fetology: Diagnosis and Management of the Fetal Patient, 2e
YR 2015
FD 2015
PB McGraw-Hill Education
PP New York, NY
SN 978-0-07-144201-5
LK obgyn.mhmedical.com/content.aspx?aid=1106398374
RD 2024/04/19
AB Key  PointsHeterotaxy  is  an  abnormality  of  formation  of  the  left–right  axis  of  the  body.Heterotaxy  refers  to  any  arrangement  that  deviates  from  situs  solitus  or  complete  situs  inversus.Left  atrial  isomerism  or  polysplenia  syndrome  usually  has  absent  right-sided  organs  and  bilaterally  placed  left-sided  organs  with  multiple  splenic  masses  along  the  greater  curvature  of  the  stomach.Right  atrial  isomerism  or  asplenia  syndrome  usually  has  bilaterally  trilobed  lungs,  globular  central  lines,  severe  congenital  heart  defects,  and  absent  spleen.Fetal  echocardiography  is  indicated  in  all  suspected  cases  of  heterotaxy.Delivery  in  a  tertiary  care  center  is  recommended.