RT Book, Section A1 Bianchi, Diana W. A1 Crombleholme, Timothy M. A1 D'Alton, Mary E. A1 Malone, Fergal D. SR Print(0) ID 1106398525 T1 Ectopia Cordis T2 Fetology: Diagnosis and Management of the Fetal Patient, 2e YR 2015 FD 2015 PB McGraw-Hill Education PP New York, NY SN 978-0-07-144201-5 LK obgyn.mhmedical.com/content.aspx?aid=1106398525 RD 2024/03/28 AB Key PointsEctopia cordis is a rare malformation in which the fetal heart is present in an extrathoracic location.It is easily diagnosable by fetal ultrasound, as early as 10 weeks of gestation.Detailed fetal echocardiography is recommended to confirm whether the internal cardiac anatomy is normal, as the prognosis is essentially lethal if associated cardiac malformations are present.Detailed general fetal sonographic anatomical evaluation and amniocentesis for fetal karyotype are recommended, because of reported associations with other malformations.If a patient chooses to continue the pregnancy and no other malformations are present, planned elective cesarean delivery at term, with immediate availability of neonatologists, pediatric surgeons and cardiac surgeons, is recommended.Postnatal survival has been rarely reported in cases in which no associated malformations are present.There have been no reported cases of recurrence of ectopia cordis.